Anesthetic management in hypoplastic left heart syndrome: A case report

Authors

  • Marina Huamán-Robles Médico Subespecialista en Anestesiología y Terapia Intensiva Cardiovascular
  • Rosina Ruiz-Roque Médico Subespecialista en Anestesiología y Terapia Intensiva Cardiovascular
  • Miluska Daniela Delgado-Flores Médico subespecialista en Anestesiología Cardiovascular
  • María Isabel Picón-Perla Cirujano Dentista especialista en Odontología Pediátrica
  • Mario J. Valladares-Garrido Médico Epidemiólogo

DOI:

https://doi.org/10.35434/rcmhnaaa.2022.152.1311

Keywords:

cardiovascular anesthesia, hypoplastic left heart syndrome, congenital heart disease

Abstract

Background: Hypoplastic left heart syndrome may appear with clinical signs immediately at birth, being responsible for neonatal deaths within the first week of life. Clinical recognition and echocardiographic findings are key to timely diagnosis and treatment. Case report: describes the anesthetic procedure of a neonate with hemodynamic instability who required emergency surgery for bilateral pulmonary banding to maintain the balance between pulmonary and near-unit systemic flow ratio, along with mechanical ventilation maneuvers, anesthetic, inotropic and adjuvant drugs to control vascular resistance and blood flow, thus achieving hemodynamic stability of the patient, which allowed him to undergo an elective Norwood Sano procedure on the fifth day, and which was tolerated with extubation 15 days after surgery. Conclusion: The right timing of the surgical indication increases the survival of patients with hypoplastic left heart syndrome.

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Author Biographies

Marina Huamán-Robles, Médico Subespecialista en Anestesiología y Terapia Intensiva Cardiovascular

1. Instituto Nacional Cardiovascular INCOR, Lima, Perú.

Rosina Ruiz-Roque, Médico Subespecialista en Anestesiología y Terapia Intensiva Cardiovascular

1. Instituto Nacional Cardiovascular INCOR, Lima, Perú.

Miluska Daniela Delgado-Flores, Médico subespecialista en Anestesiología Cardiovascular

1. Servicio de Centro Quirúrgico. Hospital Carlos Alberto Seguín Escobedo, Arequipa, Perú.

María Isabel Picón-Perla, Cirujano Dentista especialista en Odontología Pediátrica

1. Instituto Nacional Cardiovascular INCOR, Lima, Perú.

Mario J. Valladares-Garrido, Médico Epidemiólogo

1. Instituto de Evaluación de Tecnologías en Salud e Investigación – IETSI, EsSalud. Lima, Perú.
2. Universidad Norbert Weiner, Lima, Perú.

Published

2022-06-30

How to Cite

1.
Huamán-Robles M, Ruiz-Roque R, Delgado-Flores MD, Picón-Perla MI, Valladares-Garrido MJ. Anesthetic management in hypoplastic left heart syndrome: A case report. Rev. Cuerpo Med. HNAAA [Internet]. 2022 Jun. 30 [cited 2024 May 16];15(2):295-9. Available from: https://cmhnaaa.org.pe/ojs/index.php/rcmhnaaa/article/view/1311

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